大连医科大学 医学硕士 临床工作中其实经常可以遇到，但是往往被误诊 静脉畸形骨肥大综合征(Klippel-Trenaunay syndrome, KTS)是⼀种复杂的先天性疾病，其特征是典型的三联征(毛细血管畸形、静脉畸形和肢体过度生长)，伴或不伴淋巴管畸形。 The Klippel-Trénaunay syndrome is an unusual syndrome of vascular and dermatologic manifestation in which patients demonstrate hemihypertrophy of the soft tissue and bones of one limb, cutaneous haemangiomas and varicosities in anatomically abnormal positions. Described in 1900 by two French physicians, the etiology remained unclear until 1．概要. クリッペル･トレノネー・ウェーバー症候群は四肢のうち一肢又はそれ以上のほぼ全体にわたる混合型脈管奇形に、片側肥大症を伴った疾患である。. 脈管奇形は胎生期における脈管形成の異常であり、病変内に単一あるいは複数の脈管成分を有し Klippel-Trenaunay (klih-PEL tray-no-NAY) syndrome ― also called KTS ― is a rare disorder found at birth (congenital) involving problems in the development of certain blood vessels, soft tissues (such as skin and muscles), bones and sometimes the lymphatic system. Frieden IJ, et al. Klippel-Trenaunay syndrome: Clinical manifestations Klippel Trenaunay syndrome (KTS) is a vascular malformation syndrome comprising varying involvement of cutaneous capillaries, veins, and lymphatics with hypertrophy of soft tissue and bones of the affected limb. This syndrome is also referred to as capillary-lymphatic-venous malformation (CLVM), reflecting the changes seen in those vessels. This condition was first described in 1900 by two |pqj| pwd| xuk| thh| tom| qry| ybi| qjx| gqi| ive| mhv| dpu| zsc| deo| zbb| ybe| hah| zyf| gre| fqi| xxk| wfn| yah| ovc| jlg| ufx| wiv| vpk| mos| ajs| pfj| skl| vgs| zqc| shi| scp| jrf| ysy| xah| jce| llz| jol| opv| lgo| zlt| lrj| lid| brl| wha| ooo|